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Vol. 53. Issue 6.
Pages 573-579 (01 December 2000)
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Vol. 53. Issue 6.
Pages 573-579 (01 December 2000)
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Consenso sobre diagnóstico y tratamiento de las alteraciones del metabolismo hidrocarbonado en la fibrosis quística
Consensus on the diagnosis and management of cystic fibrosis related diabetes
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R. Barrio Castellanosa,
Corresponding author
rbarrio@hrc.insalud.es

Correspondencia: Unidad de Diabetes Pediátrica. Servicio de Pediatría. Hospital Ramón y Cajal. Crta. Colmenar Viejo km 9,4. 28034 Madrid
, A. Cos Blancob, E. García Garcíac, M. Gussinyé Cañadelld, J.F. Merino Torrese, M.T. Muñoz Calvof
a Servicios de Pediatrí Hospital Ramón y Cajal Hospital La Paz, Madrid.
b Hospital La Paz, Madrid.
c Hospital Carlos Haya, Málaga.
d Hospital Vall d’Hebron, Barcelona.
e Hospital La Fe, Valencia.
f Hospital Niño Jesús, Madrid
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La alteración del metabolismo hidrocarbonado es una complicación frecuente de la fibrosis quística. La diabetes relacionada con fibrosis quística (DRFQ) se debe a una disminución en la secreción de la insulina secundaria a la insuficiencia pancreática. Los pacientes con fibrosis quística y diabetes presentan mayor morbilidad y mortalidad y el mismo riesgo de las complicaciones crónicas de la diabetes que los pacientes con diabetes tipo 1o 2.

El diagnóstico precoz y el tratamiento adecuado de la diabetes de estos pacientes es imprescindible.

En mayo de 2000 tuvo lugar en Madrid una conferencia de consenso sobre DRFQ para definir las pautas para su diagnóstico y tratamiento.

Palabras clave:
Fibrosis quística
Diabetes relacionada con fibrosis quística (DRFQ)
Diabetes mellitus
Alteración de la tolerancia a la glucosa

Abnormal glucose tolerance and diabetes mellitus are a common complication of cystic fibrosis (CF). Cystic fibrosis related diabetes (CFRD) is due to decreased insulin secretion, secondary to pancreatic insufficiency. Patients with CFRD have increased morbidity and mortality and are subject to the same microvascular complications as patients with other types of diabetes. Prompt diagnosis and aggressive management of CFRD is important.

A consensus conference on CFRD was held in Madrid in May 2000 to define the current standards for the diagnosis and management of this disease in Spain.

Key words:
Cystic fibrosis
Diabetes mellitus
Impaired glucose tolerance
Cystic fibrosis related diabetes mellitus
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Copyright © 2000. Asociación Española de Pediatría
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